Diagnosis and Management of 60 Children with Congenital Vascular Rings: A 10-year Experience
نویسندگان
چکیده
IntroductIon Congenital vascular rings (VRs) are a group of rare cardiovascular anomalies that result from abnormal embryonic development of the paired aortic arches or branching pulmonary arteries. Clinical presentation of VR depends on its anatomy, degree, and site of compression. Stridor, recurrent upper respiratory tract infections and feeding difficulty were frequent symptoms of VR. Barium swallow test, echocardiography, computed tomography (CT) and magnetic resonance imaging (MRI) present as effective diagnostic tools for VR evaluation. Surgical interventions are required for symptomatic VR patients, and result in favorable outcomes in most cases. However, tracheal stenosis (TS) can often present and be the cause of surgical failure.
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